脂肪细胞肿瘤(Adipocytictumours)
良性(Benign)8850/0 脂肪瘤 NOS(Lipoma NOS) 8856/0肌内脂肪瘤(Intramuscularlipoma) - 软骨样脂肪瘤(Chondroid lipoma)
- 脂肪瘤病(Lipomatosis)
- 弥漫性脂肪瘤病(Diffuselipomatosis)
- 多发对称性脂肪瘤病(Multiplesymmetrical lipomatosis)
- 盆腔脂肪瘤病(Pelviclipomatosis)
- 类固醇脂肪瘤病 (Steroidlipomatosis)
- 艾滋病毒脂肪代谢障碍 (HIV lipodystrophy)
- 神经脂肪瘤病 (Lipomatosisof nerve)
8881/0 脂肪母细胞瘤病 (Lipoblastomatosis) - 局限性(脂肪母细胞瘤) (Localized (lipoblastoma))
- 弥漫性(脂肪母细胞瘤病) (Diffuse (lipoblastomatosis))
8861/0 血管脂肪瘤NOS(Angiolipoma NOS) - 细胞性血管脂肪瘤 (Cellularangiolipoma)
8890/0 肌脂肪瘤(Myolipoma) 8862/0 软骨样脂肪瘤(Chondroid lipoma) 8857/0 梭形细胞脂肪瘤(Spindlecell lipoma) 8857/0 非典型梭形细胞/多形性脂肪瘤样肿瘤(Atypical spindle cell/pleomorphic lipomatous tumour) 8880/0冬眠瘤(Hibernoma） 中间性(局部侵袭性)Intermediate(locally aggressive) 8850/1 非典型性脂肪瘤性肿瘤(Atypical lipomatous tumour) 恶性(Malignant)8851/3 脂肪肉瘤,高分化, NOS (Liposarcoma,well-differentiated, NOS) 8851/3 脂瘤样脂肪肉瘤(Lipoma-likeliposarcoma) 8851/3 炎性脂肪肉瘤(Inflammatoryliposarcoma) 8851/3 硬化化性脂肪肉瘤(Sclerosingliposarcoma) 8858/3 去分化脂肪肉瘤(Dedifferentiatedliposarcoma) 8852/3黏液样脂肪肉瘤(Myxoidliposarcoma) 8854/3 多形性脂肪肉瘤(Pleomorphicliposarcoma) - 上皮样脂肪肉瘤(Epithelioidliposarcoma)
8859/3 粘液样多形性脂肪肉瘤(Myxoidpleomorphic liposarcoma)
成纤维细胞/肌成纤维细胞性肿瘤(Fibroblasticand myofibroblastic tumours)
良性(Benign)8828/0结节性筋膜炎(Nodularfasciitis) - 血管内筋膜炎(Intravascularfasciitis)
- 颅筋膜炎(Cranialfasciitis)
8828/0增生性筋膜炎(Proliferativefascitis) 8828/0 增生性肌炎(Proliferativemyositis) - 骨化性肌炎和指趾纤维骨性假瘤(Myositis ossificans and fibro-osseous pseudotumourof digits)
- 缺血性筋膜炎(Ischaemicfasciitis)
8820/0弹力纤维瘤(Elastofibroma) 8992/0婴儿纤维性错构瘤(Fibroushamartoma of infancy) - 结肠纤维瘤病(Fibromatosiscolli)
- 幼年性玻璃样变纤维瘤病(Juvenilehyaline fibromatosis)
- 包涵体纤维瘤病(Inclusionbody fibromatosis)
8813/0 腱鞘纤维瘤(Fibromaof tendon sheath) 8810/0增生性纤维母细胞瘤(Desmoplasticfibroblastoma) 8825/0 肌纤维母细胞瘤(Myofibroblastoma) 8816/0钙化性腱膜纤维瘤(Calcifyingaponeurotic fibroma) - EWSRI-SMAD3阳性纤维母细胞瘤(新增)(EWSR1-SMAD3-positive fibroblastic tumour(emerging))
8826/0血管肌纤维母细胞瘤(Angiomyofibroblastoma) 9160/0 细胞性血管纤维瘤(Celularangiofibroma) 9160/0 血管纤维NOS(Angiofibroma NOS) 8810/0项型纤维瘤(Nuchalfibroma) 8811/0肢端纤维粘液瘤(Acralfibromyxoma) 8810/0 Gardner纤维瘤(Gardnerfibroma) 中间性(局部侵袭性)Intermediate(locally aggressive)8815/0 孤立性纤维性肿瘤,良性(Solitary fibrous tumour, benign) 8813/1掌跖纤维瘤病(Palmar/plantar-typefibromatosis) 8821/1韧带样纤维瘤病(Desmoid-typefibromatosis) 8821/1 腹外带样纤维瘤病(Extra-abdominaldesmoid fibromatosis) 8822/1 腹部纤維瘤病(Abdominalfibromatosis) 8851/1 脂肪纤维瘤病(Lipofibromatosis) 8834/1巨细胞纤维母细胞瘤(Giantcell fibroblastoma) 中间性(偶有转移性)Intermediate(rarelymetastasizing)8832/1 隆突性皮肤纤维肉瘤NOS(Dermatofibrosarcoma protuberans NOS) 8833/1色索性隆突性皮肤纤维肉瘤(Pigmenteddermatofibrosarcoma protuberans) 8832/3纤维肉瘤性隆突性皮肤纤维肉瘤(Dermatofibrosarcoma protuberans, fibrosarcomatous) - 黏液性隆突性皮肤纤維肉瘤(Myxoid dermatofibrosarcoma protuberans)
- 隆突性皮肤纤维肉瘤伴肌样分化(Dermatofibrosarcoma protuberans with myoid differentiation)
- 斑块样隆突性皮肤纤维肉瘤(Plaque-like dermatofibrosarcoma protuberans)
8815/1孤立性纤维性肿瘤NOS(Solitary fibrous tumour NOS) - 脂肪形成(脂防瘤性)孤立性纤维性肿瘤(Fat-forming(lipomatous) solitary fibroustumour)
- 富巨細胞性孤立性纤維性肿瘤(Giantcell-rich solitary fibrous tumour)
- 上皮样炎性肌纤维母细胞肉瘤(Epithelioid inflammatory myofibroblastic sarcoma)
8825/3 肌纤维母细胞肉瘤(Myofibroblasticsarcoma) 8810/1 CD34阳性浅表纤维母细胞瘤(Superficial CD34-positive fibroblastic tumour) 8811/1 點液炎性纤维母细胞肉瘤(Myxoinflammatoryfibroblastic sarcoma) 8814/3 婴儿纤维肉瘤(Infantilefibrosarcoma) 恶性(Malignant)8815/3孤立性纤维性肿瘤,恶性(Solitary fibrous tumour, malignant) 8810/3维肉NOS(Fibrosarcoma NOS) 8811/3 黏液性纤维肉瘤(Myxofibrosarcoma) - 上皮样點液性纤维肉瘤(Epithelioidmyxofibrosarcoma)
8840/3低度恶性纤维黏液样肉瘤(Low-gradefibromyxoid sarcoma) 8840/3 硬化性上皮样纤维肉瘤(Sclerosingepithelioid fibrosarcoma)
所谓的纤维组织细胞性肿瘤(So-called fibrohistiocytic tumours)
良性(Benign)9252/0 鞘鞘巨细胞肿瘤NOS(Tenosynovial giant cell tumour NOS) 9252/1 腱鞘巨细胞肿瘤，弥漫型(Tenosynovialgiant cell tumour, diffuse) 8831/0 深部良性纤维組织细胞瘤(Deepbenign fibrous histiocytoma) 中间性(偶有转移性)Intermediate(rarelymetastasizing)8835/1 丛状纤维组织细胞瘤(Plexiformfibrohistiocytic tumour) 9251/1 软组织巨细胞瘤(Giantcell tumour of soft parts NOS) 恶性(Malignant)9252/3 恶性鞘巨细胞瘤(Malignanttenosynovial giant cell tumour)
血管性肿瘤(Vasculartumours)
良性(Benign)9120/0 血管瘤NOS(Haemangioma NOS) 9132/0 肌内血管瘤(Intramuscularhaemangioma) 9123/0 动静詠血管(Arteriovenoushaemangioma) 9122/0 静脉型血管(Venoushaemangioma) 9125/0上皮样血管瘤(Epithelioidhaemangioma) - 细胞性上皮样血管瘤(Cellularepithelioid haemangioma)
- 非典型上皮样血管瘤(Atypicalepithelioid haemangioma)
9170/0淋巴管瘤NOS(Lymphangioma NOS) 9173/0 囊性淋巴管瘤(Cysticlymphangioma) 9161/0 获得性袢状血管瘤(Acquiredtufted haemangioma) 中间性(局部侵装性)Intermediate(locally aggressive)9130/1卡波西型血管内皮瘤(Kaposiformhaemangioendothelioma) 中间性(偶有转移性)Intermediate(rarelymetastasizing)9136/1网状血管内皮瘤(Retiformhaemangioendothelioma) 9135/1乳头状淋巴管内血管内皮瘤(Papillaryintralymphatic angioendothelioma) 9136/1 混合性血管内皮瘤(Compositehaemangioendothelioma) - 神经内分泌性混合性血管内皮瘤(Neuroendocrine composite haemangioendothelioma)
9140/3卡波西肉瘤(Kaposisarcoma) - 经典型情性卡波西肉瘤(Classicindolent Kaposi sarcoma)
- 非洲地方性卡波西肉瘤(EndemicAfrican Kaposi sarcoma)
- 艾滋病相关性卡波西肉瘤(AIDS-associatedKaposi sarcoma)
- 迟发型卡波西肉瘤(latrogenicKaposi sarcoma)
9138/1假性肌(类上皮肉瘤样)血管内皮细胞瘤(Pseudomyogenic(epithelioidsarcoma-like)haemangioendothelioma) 恶性(Malignant)9133/3 上皮样血管内皮瘤NOS(Epithelioid haemangioendothelioma NOS) - 上皮样血管内皮瘤伴WWTR1-CAMTA1融合(Epithelioid haemangioendothelioma withWWTR1-CAMTA1 fusion)
- 上皮样血管内皮瘤伴YAP1-TFE3融合(Epithelioid haemangioendothelioma withYAP1-TFE3 fusion)
9120/3 血管肉瘤(Angiosarcoma)
周细胞性(血管周细胞性)肿瘤(Pericytic(perivascular)tumours)
良性和中间性(Benignand intermediate)8711/0 血管球瘤NOS(Glomus tumour NOS) 8712/0 血管球瘤(Glomangioma) 8713/0 血管球肌瘤(Glomangiomyoma) 8711/1 血管球瘤病(Glomangiomatosis) 8711/1 恶性潜能不确定性血管球肿瘤(Glomus tumour of uncertain malignant potential) 8824/0肌周细胞瘤(Myopericytoma) 8824/1 肌纤维瘤病(Myofibromatosis) 8824/0肌纤维瘤(Myofibroma) 8824/1 婴儿性肌纤维瘤病(Infantilemyofibromatosis) 8894/0血管平滑肌瘤(Angioleiomyoma) 恶性(Malignant)8711/3恶性血管球(Glomustumour, malignant)
骨肌肿瘤(Skeletalmuscle tumours)
良性(Benign)8900/0横纹肌NOS(Rhabdomyoma NOS) 8903/0 胎儿型横纹肌瘤(Fetalrhabdomyoma) 8904/0 成人型横纹肌瘤(Adultrhabdomyoma) 8905/0 生殖道型横纹肌瘤(Genitalrhabdomyoma) 恶性(Malignant)8910/3 胚胎性横纹肌肉瘤NOS(Embryonal rhabdomyosarcoma NOS) 8910/3 胚胎性横纹肌肉瘤,多形性(Embryonal rhabdomyosarcoma,pleomorphic) 8920/3 腺泡状横纹肌肉瘤(Alveolarrhabdomyosarcoma) 8901/3 多形性横纹肌肉NOS(Pleomorphic rhabdomyosarcoma NOS) 8912/3梭形细胞性横纹肌肉瘤(Spindlecell rhabdomyosarcoma) - 先天性梭形细胞横纹肌肉瘤伴VGLL2/NCOA2/CITED2重排(Congenital spindle cellhabdomyosarcoma withVGLL2/NCOA2/CITED2 rearrangements)
- MYOD1-突变梭形细胞性/硬化性横纹肌肉瘤(MYOD1-mutant spindle cell/sclerosing rhabdomyosarcoma)
- 骨内梭状细胞横纹肌肉瘤(伴TFCP2/NCOA2重排)(Intraosseous spindle cell rhabdomyosarcoma (withTFCP2/NCOA2 rearrangements))
8921/3 外胚层间叶瘤(Ectomesenchymoma)
胃肠道间质瘤(Gastrointestinalstromal tumours)8936/3胃肠道间质瘤(Gastrointestinalstromal tumour)
软骨-骨性肿瘤(Chondro-osseoustumours)
良性(Benign)9220/0 软骨瘤NOS(Chondroma NOS) - 软骨母细胞瘤样软组织软骨瘤 (Chondroblastoma-likesoft tissue chondroma)
9180/3 骨外骨肉瘤(Osteosarcoma,extraskeletal)
周围神经鞘肿瘤(Peripheralnerve sheath tumours)
良性(Benign)9560/0 神经鞘瘤NOS(Schwannoma NOS) 9560/0 陈旧性神经鞘瘤(Ancientschwannoma) 9560/0 细胞性神经鞘瘤(Cellularschwannoma) 9560/0 丛状神经鞘(Plexiformschwannoma) - 上皮样神经鞘瘤(Epithelioidschwannoma)
- 微囊/网状神经鞘瘤(Microcystic/reticularschwannoma)
9540/0 神经纤维瘤NOS(Neurofibroma NOS) - 陈旧神经纤维瘤(Ancientneurofibroma)
- 细胞性神经纤维瘤(Cellularneurofibroma)
- 非典型神经纤维瘤(Atypicalneurofibroma)
9550/0 丛状神经纤维瘤(Plexiformneurofibroma) 9571/0 神经束膜瘤NOS(Perineurioma NOS) - 网状神经束膜瘤(Reticularperineurioma)
- 硬化性神经東膜瘤(Sclerosingperineurioma)
9580/0颗粒细胞瘤NOS(Granular cell tumour NOS) 9562/0 神经鞘黏液瘤(Nervesheath myxoma) 9570/0孤立性局限性神经瘤(Solitarycircumscribed neuroma) - 丛状孤立性局限性神经瘤(Plexiformsolitary circumscribed neuroma)
9530/0 脑膜NOS(Meningioma NOS) - 良性蝾螈瘤/神经肌肉性迷芽瘤(Benign triton tumour /neuromuscular choristoma)
9563/0 混杂性神经鞘瘤(Hybridnerve sheath tumour) - 神经束膜瘤/神经鞘瘤(Perineurioma/schwannoma)
- 神经鞘瘤/神经纤维瘤(Schwannoma/neurofibroma)
- 神经束膜瘤/神经纤维瘤(Perineurioma/neurofibroma)
9540/3恶性周神经鞘膜瘤NOS(Malignant peripheral nerve sheath tumour NOS) 9542/3上皮样恶性周围神经鞘膜瘤(Malignant peripheral nerve sheath tumour,epithelioid) 9540/3黑色素性恶性周围神经鞘膜瘤(Melanotic malignant peripheral nerve sheathtumour) 9580/3恶性颗粒细胞瘤(Granularcell tumour, malignant) 9571/3 恶性神经鞘瘤(Perineurioma,malignant)
未确定分化的肿瘤(Tumours of uncertain differentiation)
良性(Benign)8840/0 黏液瘤NOS(Myxoma NOS) 8841/0 侵袭性血管黏液瘤(Aggressiveangiomyxoma) 8802/1 多形性透明变性血管扩张性肿瘤(Pleomorphic hyalinizing angiectatic tumour) 8990/0 磷酸盐尿性间叶性肿瘤NOS(Phosphaturic mesenchymal tumour NOS) 8714/0 良性血管周围上皮样瘤(Perivascularepithelioid tumour, benign) 8860/0血管平滑肌脂肪瘤(Angiomyolipoma) 中间性(局部侵袭性)Intermediate(locally aggressive)8811/1 含铁血黄素沉着性纤维脂肪瘤性肿瘤(Haemosiderotic fibrolipomatous tumour) 8860/1 上皮样血管平滑肌脂肪瘤(Angiomyolipoma,epithelioid) 中间性(偶有转移性)Intermediate(rarelymetastasizing)8830/1 非典型纤维黄色瘤(Atypicalfibroxanthoma) 8842/0 骨化性纤维黏液样瘤(Ossifyingfibromyxoid tumour NOS) 8940/0 混合NOS(Mixed tumour NOS) 8940/3 性混合NOS(Mixed tumour, malignant,NOS) 8982/0 肌上皮瘤NOS(Myoepithelioma NOS) 恶性(Malignant)8990/3恶性磷酸盐尿性间叶性肿瘤(Phosphaturic mesenchymal tumour, malignant) - NTRK重排的梭形细胞肿瘤(新出现)(NTRK-rearranged spindle cell neoplasm(emerging))
9040/3 滑膜肉NOS(Synovial sarcoma NOS) 9041/3 滑膜肉瘤，梭形细胞型(Synovialsarcoma, spindle cell) 9043/3 滑膜肉瘤，双相型(Synovialsarcoma, biphasic) - 滑膜肉瘤，低分化型(Synovialsarcoma, poorly differentiated)
8804/3上皮样肉瘤(Epithelioidsarcoma) - 近端或大细胞型上皮样肉瘤(Proximalor large cell epithelioid sarcoma)
- 典型样上皮样肉瘤(Classicepithelioid sarcoma)
9581/3 腺泡状软组织肉瘤(Alveolarsoft part sarcoma) 9044/3软组织透明细胞肉瘤(Clearcell sarcoma NOS) 9231/3 骨外黏液样软骨肉瘤(Extraskeletalmyxoid chondrosarcoma) 8806/3促结缔组织增生性小圆细胞肿瘤(Desmoplasticsmall round cell tumour) 8963/3 横纹肌样瘤(Rhabdoidtumour NOS) 8714/3 恶性血管周围上皮样肿瘤(Perivascularepithelioid tumour, malignant) 9137/3血管内膜肉瘤(Intimalsarcoma) 8842/3骨化性纤维黏液样肿瘤，恶性(Ossifying fibromyxoid tumour, malignant) 8982/3 肌上皮癌(Myoepithelialcarcinoma) 8805/3 未分化肉瘤(Undifferentiatedsarcoma) 8801/3梭形细胞肉瘤，未分化 (Spindlecell sarcoma, undifferentiated) 8802/3多形性肉瘤，未分化(Pleomorphicsarcoma, undifferentiated) 8803/3圆形细胞肉瘤，未分化(Roundcell sarcoma, undifferentiated)
参考文献
2020年第五版WHO软组织肿瘤分类
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